Diabetes Mellitus in Pediatric Patients with Cystic Fibrosis

Authors

DOI: https://doi.org/10.6018/eglobal.18.2.347521
Keywords: Cystic Fibrosis, Diabetes Mellitus, new-born, child, quality of life

Abstract

Introduction: Cystic Fibrosis (CF) is a hereditary recessive disease that affects several organs, mainly within the respiratory and digestive systems. Cystic Fibrosis Related Diabetes (CFRD) is one of its main complications.
Objectives: To study the specific complications of pediatric patients suffering from CFRD and how they affect a patient’s quality of life. To compare the mortality rates of pediatric patients with CF and with CFRD. To highlight the importance of nurses in the management of pediatric patients with CFRD.
Methodology: A systematic bibliographic review was conducted. We included studies, in English and Spanish, published over the last 10 years, which analysed a population aged between 0 and 9 years old with CF and/or CFRD.
Results: Four databases were used for the systematic search. We analysed 10 articles to address the objectives.
Conclusions: The complications caused by CFRD and the care that patients require affect the patient’s quality of life. Progress both with diagnosis and with treatment has improved the quality of life of patients, and has contributed to reductions in the difference between the mortality rates of patients with CF and without CFRD. Nurses who care for children with CFRD are essential as an information resource for patients and their families. Nurses must convey the importance of therapeutic adherence to achieve a better quality of life.

 

Downloads

Download data is not yet available.

Author Biography

Diego Serrano-Gómez, University of Burgos

Diego Serrano-Gómez: Doctor en Biología, actualmente es el Secretario Académico de la Facultad de Ciencias de la Salud e imparte clases de Farmacología, Metodología de la Investigación y coordina los TFG de Enfermería. Ha desempeñado puestos de gestión de la investigación científica en el Instituto Aragonés de Ciencias de la Salud de Zaragoza, y ha trabajado como investigador en el CSIC y en la Universidad de Vermont (USA). Pertenece al grupo de innovación docente Blended- Learning en Ciencias de la Salud (B-LCS), de la Universidad de Burgos

References

Las ER [Internet]. CRE Enfermedades Raras. Centro de Referencia Estatal de Atención a Personas con Enfermedades Raras y sus Familias de Burgos. 2015. Available from: http://www.creenfermedadesraras.es/creer_01/er_mh/er/index.htm

¿Qué es la Fibrosis Quística? [Internet]. Federación Española de Fibrosis Quística. 2015. Available from: https://fibrosisquistica.org/?pagina=fibrosi

Escobar Héctor, Sojo A. Fibrosis quística: protocolos diagnósticos y terapéuticos en pediatría. :99–110. Available from: http://www.aeped.es/sites/default/files/documentos/10-FQ.pdf

Omneda. Fibrosis quística Síntomas: Pulmones, Páncreas, Aparato digestivo, Bilis [Internet]. Onmeda. 2017. Available from: http://www.onmeda.es/enfermedades/fibrosis_quistica-sintomas-1568-4

Acuña Quirós MD, Araque González S, Azxorra Liñero I, Castillo Calcerrada J, Costilla García A, Girón Moreno R, et al. Guía de apoyo y cuidados para enfermos y familiares con Fibrosis Quística. Lo que necesitan el paciente y su familia. 2017.

Tratamiento [Internet]. Federación Española de Fibrosis Quística. 2015. Available from: https://fibrosisquistica.org/?pagina=vivir&vivir=tratamiento

Sánchez-Solis de querol M, Baquero Mochales F, Cantón Moreno R, Gartner Tizzano S, Cobos Barroso N, Salcedo Posadas A, et al. Los tres pilares del tratamiento en fibrosis quística. Federación Española contra la Fibosis Quística. Valencia; 2014.

Diagnóstico [Internet]. Federación Española de Fibrosis Quística. 2015. Available from: https://fibrosisquistica.org/?pagina=vivir&vivir=diagnostico

SaCyL. Programa de detección precoz de enfermedades congénitas [Internet]. Junta de Castilla y León. 2018. Available from: http://www.saludcastillayleon.es/profesionales/es/programas-guias-clinicas/programas-salud/programa-deteccion-precoz-enfermedades-congenitas

Escobar Castro H, Sojo Aguirre A, Gil Ortega D, Nadal Ortega JM. Fibrosis quística. Asoc Española Pediatría [Internet]. 2010;77–84. Available from: http://www.aeped.es/sites/default/files/documentos/fquistica.pdf

Alonso M, Barrio R, Martín-Frías M, Álvare MÁ, Yelmo R, Martínez E, et al. Lo que debes saber sobre la Diabetes Relacionada con la Fibrosis Quística (DRFQ) [Internet]. Madrid: Federación Española de Fibrosis Quística; 2014. Available from: https://www.seep.es/images/site/gruposTrabajo/enlaces/Diabetes_en_Fibrosis_Quistica-RB.pdf

Brunzell C, S. Hardin D, Kogler A, Moran A, Schindler T. El manejo de la Diabetes Relacionada con la Fibrosis Quística (CFRD): Una guía instructiva para los pacientes y sus familias [Internet]. 6a. Bethesda: Cystic Fibrosis Foundation; 2015. Available from: https://www.cff.org/Spanish-Language-CFRD-Manual.pdf

Laguna TA, Nathan BM, Moran A. Managing diabetes in cystic fibrosis. Diabetes, Obes Metab. 2010;12:858–64.

O’Riordan SMP, Robinson PD, Donaghue KC, Moran A. Management of cystic fibrosis-related diabetes in children and adolescent. Pediatr Diabetes. 2009;10:43–50.

Ode KL, Moran A. New insights into cystic fibrosis-related diabetes in children. Lancet Diabetes Endocrinol. 2013;1:52–8.

Moran A, Brunzell C, Cohen RC, Katz M, Marshall BC, Onady G, et al. Clinical Care Guidelines for Cystic Fibrosis-Related Diabetes. Diabetes Care. 2010;33:2697–708.

Cohen-Cymberknoh M, Shoseyov D, Kerem E. Managing Cystic Fibrosis. Am J Respir Crit Care Med. 2011;183:1463–71.

Kelly A, Moran A. Update on cystic fibrosis-related diabetes. J Cyst Fibros. 2013;12:318–31.

Chamnan P, Shine BSF, Aworth CS, Bilton D, Adler AI. Diabetes as a Determinant of Mortality in Cystic Fibrosis. Diabetes Care. 2010;33:311–6.

O’Riordan SMP, Dattani MT, Hindmarsh PC. Cystic Fibrosis-Related Diabetes in Childhood. Horm Res Oaediatrics. 2010;73:15–24.

Moran A, Dunitz J, Nathan B, Saeed A, Holme B, Thomas W. Cystic Fibrosis-Related Diabetes: Current Trends in Prevalence, Incidence, and Mortality. Diabetes Care. 2009;32:1626–31.

Illán Noguera CR, Álvarez Martínez M del C, Martínez Rabadán M, Pina Díaz LM, Guillén Pérez F, Bernal Barquero M, et al. Cuidados de enfermería y orientación en niños y adolescentes con fibrosis quística: una revisión bibliográfica. Rev Enfermería Docente. 2014;102:67–74.

Published
08-03-2019
How to Cite
[1]
Álvarez Ortega, S. and Serrano-Gómez, D. 2019. Diabetes Mellitus in Pediatric Patients with Cystic Fibrosis. Global Nursing. 18, 2 (Mar. 2019), 533–562. DOI:https://doi.org/10.6018/eglobal.18.2.347521.
Issue
Section
REVIEWS